Melibiase

• Enzyme replacement

• Agalsidase alfa
• Alpha-D- galactoside galactohydrolase
• Alpha-D-galactosidase A
• Alpha-galactosidase A precursor
• Melibiase
• Fabrazyme (Genzyme Corp)

• No information avaliable

C₂₀₂₉H₃₀₈₀N₅₄₄O₅₈₇S₂₇

http://www.rxlist.com/cgi/generic3/fabrazyme.htm

No information avaliable

45351.6

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Liquid

-0.307

Powder for solution

For treatment of Fabry's disease (alpha-galactosidase A deficiency)

Used in the treatment of Fabry disease, an X-linked genetic disorder of glycosphingolipid metabolism. The disease is characterized by a deficiency of the lysosomal enzyme alpha-galactosidase A, which leads to progressive accumulation of glycosphingolipids, predominantly GL-3, in many body tissues. Clinical manifestations of Fabry disease include renal failure, cardiomyopathy, and cerebrovascular accidents. Fabrazyme is intended to provide an exogenous source of alpha-galactosidase A and to limit the accumulation of these glycolipids in the tissues.

No information avaliable

No information avaliable

BIOD00075.html

Humans and other mammals